Volume 4, Issue 1, June 2018, Page: 4-10
Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis
Cárcamo Idiáquez Osmar Adán, Maxillofacial Surgery Department, Meritorious Autonomous University of Puebla, Puebla, Mexico
Cortes Flores Michelle, Maxillofacial Surgery Department, Mexican Institute of Social Security, Guadalajara, Mexico
Anchecta Castro Diana Marielos, Faculty of Stomatology, Meritorious Autonomous University of Puebla, Puebla, Mexico
Vivanco Pérez Israel, Maxillofacial Surgery Department, Meritorious Autonomous University of Puebla, Puebla, Mexico
Navarro Zarate Adolfo, Maxillofacial Surgery Department, Meritorious Autonomous University of Puebla, Puebla, Mexico
Received: Jan. 31, 2018;       Accepted: Feb. 16, 2018;       Published: Mar. 19, 2018
DOI: 10.11648/j.ijcoms.20180401.12      View  1780      Downloads  68
Abstract
Fibrodysplasia Ossificans Progressiva (FOP) is a connective tissue disorder that progressively affects tendons, ligaments, aponeurosis, fasciae and muscles which undergo fibrous cell proliferation that progresses to mature bone. It has a prevalence of 1 case per 2 million habitants, having reported less than 1000 cases worldwide. In the maxillofacial region, it might originate extra-articular temporomandibular ankylosis by ossification of ligaments, muscles of the mastication, head and a neck muscles; the most commonly affected are the masseters and sternocleidomastoids. The purpose of this article is to review the Fibrodysplasia Ossificans Progressiva (FOP) and to present the case of a 12-year-old male patient with FOP that causes extra-articular temporomandibular ankylosis. There is no effective proven treatment or prevention and the life expectancy of these patients approaches the 40 years of age, so the management of patients with FOP must be performed with a multidisciplinary approach in which the various health professionals work in a coordinated and joint way to offer a better quality of life to these patients and thus better understand the progression of the disease.
Keywords
Fibrodysplasia Ossificans Progressiva, Myositis Ossificans Systemic, Munchmeyer's Disease, Extra-Articular Temporomandibular Ankylosis, Ankylosis of the Temporomandibular Joint
To cite this article
Cárcamo Idiáquez Osmar Adán, Cortes Flores Michelle, Anchecta Castro Diana Marielos, Vivanco Pérez Israel, Navarro Zarate Adolfo, Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis, International Journal of Clinical Oral and Maxillofacial Surgery. Vol. 4, No. 1, 2018, pp. 4-10. doi: 10.11648/j.ijcoms.20180401.12
Copyright
Copyright © 2018 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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